IN THIS ISSUE

Adult Congenital Heart Update


FEATURED GUEST EDITOR See More

ISSUE INTRO

The Growing Number of Adults Surviving with Congenital Heart Disease

MacGillivray TM, Lin CH. The Growing Number of Adults Surviving with Congenital Heart Disease. Methodist DeBakey Cardiovasc J. 2019;15(1):97-8.

RECOGNITIONS

Drs. MacGillivray and Lin Take the Lead in Adult Congenital Heart Disease

Drs. MacGillivray and Lin Take the Lead in Adult Congenital Heart Disease. Methodist DeBakey Cardiovasc J. 2009;15(2):96.

REVIEW ARTICLES See More

Advanced Cardiac Imaging for Complex Adult Congenital Heart Diseases

Malahfji M, Chamsi-Pasha MA. Advanced Cardiac Imaging for Complex Adult Congenital Heart Diseases. Methodist DeBakey Cardiovasc J. 2019;15(2):99-104.

149 Fontan Conversions

Backer CL, Mavroudis C. 149 Fontan Conversions. Methodist DeBakey Cardiovasc J. 2019;15(2):105-10.

Anomalous Aortic Origin of a Coronary Artery

Molossi S, Martínez-Bravo LE, Mery CM. Anomalous Aortic Origin of a Coronary Artery. Methodist DeBakey Cardiovasc J. 2019;15(2):111-21.

Pulmonary Valve Replacement for Tetralogy of Fallot

Balzer D. Pulmonary Valve Replacement for Tetralogy of Fallot. Methodist DeBakey Cardiovasc J. 2019;15(2):122-32.

Management of the Adult with Arterial Switch

Dextro-transposition of the great arteries (d-TGA) is a lethal congenital heart defect in which the great arteries—the pulmonary artery and aorta—are transposed to create ventriculoarterial discordance. Corrective surgical interventions have resulted in significant improvements in morbidity and mortality for this once-fatal congenital heart defect. The initial palliative surgery for d-TGA was the atrial switch operation, which provided physiological correction. The Mustard and Senning “atrial switch” procedures, in which an atrial baffle is created to produce a discordant atrioventricular connection on the existing discordant ventriculoarterial connection, showed preliminary success for the correction of d-TGA. However, follow-up evaluations demonstrated increasing complications from the right ventricle utilized as a systemic ventricle, resulting in progressive right ventricular dysfunction. Thus, the search continued for an anatomical correction of d-TGA to return the great arteries to their normal ventricular connections. The arterial switch operation (ASO), though attempted and theorized by many, was first successfully performed by Dr. Jatene and colleagues in 1975. For ASO, the distal main pulmonary artery and the distal ascending aorta are transected and then anastomosed to their respective ventricles with relocation of the coronary arteries to the neoaorta. The ASO has replaced the atrial switch operation since the 1980s and is now the standard surgical correction for d-TGA. As more patients who have undergone ASO are living into adulthood, late complications of this procedure have become more evident. The most common late postoperative complications include coronary artery stenosis, neoaortic root dilation, neoaortic insufficiency, and neopulmonic stenosis. Adults who have undergone ASO in childhood will need follow-up with surveillance imaging and evaluation of new symptoms or declining function to prevent and manage late postoperative complications. This review describes the management strategies for common late complications in patients who have undergone ASO.

Ebstein’s Anomaly

Holst KA, Connolly HM, Dearani JA. Ebstein's Anomaly. Methodist DeBakey Cardiovasc J. 2019;15(2):138-44.

Heart Transplantation in Adults with Congenital Heart Disease

Fynn-Thompson F. Heart Transplantation in Adults with Congenital Heart Disease. Methodist DeBakey Cardiovasc J. 2019;15(2):145-8.

CASE REPORTS See More

Simultaneous Transfemoral Mitral and Tricuspid Valve in Ring Implantation: First Case Report with Edwards Sapien 3 Valve

Beg F, Dadu RT, Reardon MJ, Little SH, Kleiman NS, Barker CM. Simultaneous Transfemoral Mitral and Tricuspid Valve in Ring Implantation: First Case Report with Edwards Sapien 3 Valve. Methodist DeBakey Cardiovasc J. 2019;15(2):149-51.

Uneventful Follow-Up 2 Years after Endovascular Treatment of a High Flow Iatrogenic Aortocaval Fistula Causing Pulmonary Hypertension and Right Heart Failure

Petrov I, Tasheva I, Stankov Z, Polomski P, Georgieva G, Marinov K. Uneventful Follow-Up 2 Years after Endovascular Treatment of a High Flow Iatrogenic Aortocaval Fistula Causing Pulmonary Hypertension and Right Heart Failure. Methodist DeBakey Cardiovasc J. 2019;15(2):152-5.

MUSEUM OF HMH MULTIMODALITY IMAGING CENTER See More

Do I Look Fat in This? Multimodality Imaging Findings of a Cardiac Lipoma

Al-Sabeq B, Autry K, Nabi F. Do I Look Fat in This? Multimodality Imaging Findings of a Cardiac Lipoma. Methodist DeBakey Cardiovasc J. 2019;15(2):156-7.

CLINICAL PERSPECTIVES See More

The Kidney in Congenital Cyanotic Heart Disease

Lee BJ. The Kidney in Congenital Cyanotic Heart Disease. Methodist DeBakey Cardiovasc J. 2019;15(2):158-9.

EDITORIALS

Letter to the Editor in Response to “Cardiac Autonomic Neuropathy in Diabetes Mellitus”

Chhabra L, Goyal A, Prabahakar Y, Khalid N. Letter to the Editor in Response to “Cardiac Autonomic Neuropathy in Diabetes Mellitus”. Methodist DeBakey Cardiovasc J. 2019;15(2):164.

Answering the Call